Journal of Anesthesiology and Pain

ABSTRACT:

Aims and background: Osteogenesis imperfecta is an authosomal dominant disease that almost always involve the   connective tissues .The major problem in these patients is inability to synthesize collagen type -1, that leads to multiple long bone fractures. This case report is going to describe management of anesthesia in a  patient with Osteogenesis imperfecta, who was scheduled for tibia plate insertion. Following failure of spinal anesthesia, the method was changed to general anesthesia by LMA insertion.

Case report: A  45 years old man , with 35 kg  weight and 132 cm height as a known case of osteogenesis  imperfecta ,was  candidate for tibia plate insertion surgery. He could not walk  due to the severity of his disease. The bad anatomy of the mandible and its protrusion that was combined by severe congenital scoliosis, made the supine position impossible, so the patient was candidate for regional and spinal anesthesia, actually .After failure of spinal anesthesia the method was changed to general anesthesia with total intravenous anesthesia(TIVA ) and laryngeal mask(LMA ) insertion for airway management. Management of anesthesia was good and patient was discharged from hospital healthy, after 3 days.