TY - JOUR JF - jap JO - JAP VL - 2 IS - 3 PY - 2011 Y1 - 2011/10/01 TI - Case Report: Anesthesia management for hysterotomy in a case of Morquio's syndrome  TT - گزارش مورد: گزارش اداره ی بیهوشی جهت انجام هیستروتومی در یک موردسندرم مورکیو N2 - Morquio's syndrome is an autosomal recessive disease. It is from mucopolysacaridosis group disease and it's obvious clinical signs are severe skeletal dysplasia and normal intelligence. Deposition of keratan sulfate in different tissues is seen and with progression of the disease, connective tissue of cornea, airways, lung and heart valves will be involved. In this article we present a case of Morquio's rare syndrome that we terminated the pregnancy due to severe respiratory distress of mother and also we present the anesthesia management of this case. SP - 69 EP - 74 AU - Almasi-nokiani, Fariba AU - Rahimzadeh, Poupak AU - Faiz, Hamid-reza AU - Akbari, Hossein AU - Almasi, Ali-reza AU - Asadolah, Sara AD - KW - Anesthesia KW - pregnancy KW - Morquio syndrome UR - http://jap.iums.ac.ir/article-1-68-en.html ER -